Journal of Pediatric Cardiology and Cardiac Surgery

The prognosis in cases of right atrial isomerism with obstructed total anomalous pulmonary venous connection remains unsatisfactory. In particular, mortality following surgical repair of obstructed total anomalous pulmonary venous connection in the neonatal period is high. This case report describes a patient who underwent primary drug-eluting stent implantation for treatment of obstructed total anomalous pulmonary venous connection associated with right atrial isomerism. The stent was placed on the day of birth, and a definitive Fontan procedure was performed at 16 months of age. We also discuss the stent specimen, which had been implanted in the vertical vein for a total of 5 months. To our knowledge, this case report is the first to describe a drug-eluting stent specimen implanted in a draining vein associated with right atrial isomerism.