Journal of Pediatric Cardiology and Cardiac Surgery

Online ISSN: 2433-1783 Print ISSN: 2433-2720
Japanese Society of Pediatric Cardiology and Cardiac Surgery
Japanese Society of Pediatric Cardiology and Cardiac Surgery Academy Center, 358-5 Yamabuki-cho, Shinju-ku, Tokyo 162-0801, Japan
Journal of Pediatric Cardiology and Cardiac Surgery 7(1): 31-35 (2023)

Case ReportCase Report

Successful Staged Repair for Isolated Pulmonary Artery of Ductal Origin: A Report of Two Cases

Department of Pediatric Cardiovascular Surgery, National Cerebral and Cardiovascular Center ◇ Osaka, Japan

受付日:2022年4月1日Received: April 1, 2022
受理日:2022年6月9日Accepted: June 9, 2022
発行日:2023年3月31日Published: March 31, 2023

Isolated pulmonary artery of ductal origin (IPADO) is a rare congenital cardiovascular disease. We describe two patients with IPADO who were successfully treated with staged repair. The first patient with left IPADO and a closing duct underwent left original Blalock–Taussig shunt at 2 months of age, then, at 11 months old, the left pulmonary artery (PA) was connected to the main PA utilizing the subclavian arterial tissues with anterior augmentation placing an autologous pericardial patch. Right-to-left lung perfusion ratio was 2.05 postoperatively. The second patient with right IPADO and a closed duct underwent right modified Blalock–Taussig shunt (a 3 mm expanded polytetrafluoroethylene tube) at 29 days of age. The right PA was connected to the main PA at 5 months of age using a flap of the main PA wall and an autologous pericardial patch for anterior augmentation. Postoperative right-to-left lung perfusion ratio was 1.14. Staged repair provided balanced distribution of blood flow to the lungs. Reconstruction of the affected PA with the patient’s own vascular tissues, instead of prosthetic materials, was feasible, promising lifetime potential of growth.

Key words: isolated pulmonary artery of ductal origin; ductal origin of a pulmonary artery; congenitally disconnected pulmonary artery; absent pulmonary artery staged repair

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