Journal of Pediatric Cardiology and Cardiac Surgery

Congenital bronchial atresia is a rare malformation that causes recurrent lung infections and pneumothorax. Pulmonary hypertension has not been reported as a complication in pediatric population, to the best of our knowledge. Our present patient is a 2-year-old girl with left pulmonary emphysema and pulmonary hypertension. She received pulmonary vasodilators and underwent left upper lobectomy. Pulmonary vasodilators were only partially effective; lobectomy was ineffective for pulmonary hypertension. Six years later after lobectomy, the patient was still receiving pulmonary vasodilators, and her pulmonary hypertension was gradually improving.